Skip Header

You are using a version of browser that may not display all the features of this website. Please consider upgrading your browser.
1 to 25 of 174  Show
Columns

UniProtKB Results

Entry
Entry name
Protein names
Gene names
Organism
Length
e
P54098DPOG1_HUMAN
DNA polymerase subunit gamma-1
POLG MDP1, POLG1, POLGA
Homo sapiens (Human)1,239
P12235ADT1_HUMAN
ADP/ATP translocase 1
SLC25A4 ANT1
Homo sapiens (Human)298
Q96RR1PEO1_HUMAN
Twinkle protein, mitochondrial
TWNK C10orf2, PEO1
Homo sapiens (Human)684
P39210MPV17_HUMAN
Protein Mpv17
MPV17
Homo sapiens (Human)176
O95571ETHE1_HUMAN
Persulfide dioxygenase ETHE1, mitoc...
ETHE1 HSCO
Homo sapiens (Human)254
Q96IL0COA8_HUMAN
Cytochrome c oxidase assembly facto...
COA8 APOP1, APOPT1, C14orf153
Homo sapiens (Human)206
Q9H845ACAD9_HUMAN
Complex I assembly factor ACAD9, mi...
ACAD9
Homo sapiens (Human)621
Q9Y276BCS1_HUMAN
Mitochondrial chaperone BCS1
BCS1L BCS1
Homo sapiens (Human)419
O95831AIFM1_HUMAN
Apoptosis-inducing factor 1, mitoch...
AIFM1 AIF, PDCD8
Homo sapiens (Human)613
Q6DKK2TTC19_HUMAN
Tetratricopeptide repeat protein 19...
TTC19
Homo sapiens (Human)380
Q15526SURF1_HUMAN
Surfeit locus protein 1
SURF1 SURF-1
Homo sapiens (Human)300
P00846ATP6_HUMAN
ATP synthase subunit a
MT-ATP6 ATP6, ATPASE6, MTATP6
Homo sapiens (Human)226
Q7KZN9COX15_HUMAN
Cytochrome c oxidase assembly prote...
COX15
Homo sapiens (Human)410
Q14249NUCG_HUMAN
Endonuclease G, mitochondrial
ENDOG
Homo sapiens (Human)297
A6NFY7SDHF1_HUMAN
Succinate dehydrogenase assembly fa...
SDHAF1 LYRM8
Homo sapiens (Human)115
Q96BR5COA7_HUMAN
Cytochrome c oxidase assembly facto...
COA7 C1orf163, RESA1, SELRC1
Homo sapiens (Human)231
P10606COX5B_HUMAN
Cytochrome c oxidase subunit 5B, mi...
COX5B
Homo sapiens (Human)129
Q9CR68UCRI_MOUSE
Cytochrome b-c1 complex subunit Rie...
Uqcrfs1
Mus musculus (Mouse)274
P47985UCRI_HUMAN
Cytochrome b-c1 complex subunit Rie...
UQCRFS1
Homo sapiens (Human)274
Q16637SMN_HUMAN
Survival motor neuron protein
SMN1 SMN, SMNT
SMN2 SMNC
Homo sapiens (Human)294
Q96RL7VP13A_HUMAN
Vacuolar protein sorting-associated...
VPS13A CHAC, KIAA0986
Homo sapiens (Human)3,174
P02766TTHY_HUMAN
Transthyretin
TTR PALB
Homo sapiens (Human)147
O75880SCO1_HUMAN
Protein SCO1 homolog, mitochondrial
SCO1 SCOD1
Homo sapiens (Human)301
Q9Y6M9NDUB9_HUMAN
NADH dehydrogenase [ubiquinone] 1 b...
NDUFB9 LYRM3, UQOR22
Homo sapiens (Human)179
Q5JTZ9SYAM_HUMAN
Alanine--tRNA ligase, mitochondrial
AARS2 AARSL, KIAA1270
Homo sapiens (Human)985
1 to 25 of 174  Show
UniProt is an ELIXIR core data resource
Main funding by: National Institutes of Health

We'd like to inform you that we have updated our Privacy Notice to comply with Europe’s new General Data Protection Regulation (GDPR) that applies since 25 May 2018.

Do not show this banner again